Patients with CF are generally managed in regional CF centres. They should be managed according to agreed protocols and advice should be sought from the centre as soon as is practical when these patients present to the ED.

Adult patients with CF are likely to be familiar with their symptoms and when they are clinically worsening – listen to their concerns as they are likely to be right about their diagnosis and treatment. They will often carry an “Alert card” indicating that they have CF and any specific pertinent issues related to their illness.

Many patients will have access ports, as IV access is sometime difficult. These should not be accessed other than by trained staff with the appropriate equipment. Establish alternate IV access if necessary.

Learning Bite

TIVADs should only be accessed by staff that are trained to do so.