Incidence and Epidemiology

The spontaneous presentation of phaeochromocytoma is normally between the age of 40–50 years, however the hereditary forms often present in younger individuals, including children [2].

About 15% of phaeochromocytomas are extra-adrenal [3].  Surgical treatment can effectively cure phaeochromocytoma in 90% of cases [4]. 

Phaeochromocytoma is associated with Von Hippel Landau disease, multiple endocrine neoplasia type 2 and neurofibromatosis type 1 [5].